一般信息 / General Information
|
目录号 |
R17007M3C11 |
|
克隆号 |
3C11 |
|
抗体类型 |
Rabbit IgG |
|
实验应用 |
ELISA, WB |
|
推荐稀释比例 |
WB 1ug/ml |
|
种属反应性 |
Human Frataxin |
|
免疫原 |
Full length recombinant human Frataxin Protein |
|
存储缓冲液 |
0.22 µM filtered solution of PBS,0.09% NaN3, pH 7.4 |
背景 / Background
FRATAXIN (FXN) is a mitochondrial protein which belongs to the FRATAXIN family. FXN regulates mito-chondrial iron transport and respiration and promotes the biosynthesis of heme and assembly and repair of iron-sulfur clusters by delivering Fe(2+) to proteins involved in these pathways. The expansion of intronic trinucleotide repeat GAA from 8-33 repeats to >90 repeats results in Friedreich ataxia. Alternative splicing results in multiple transcript variant
图片 / Picture
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存储条件 / Storage
Shipped at 4°C. Store at +4°C short term (2-4 weeks). Upon delivery aliquot. Store at -20°C or -80°C. Avoid freeze / thaw cycle.
缩略语 / Abbreviations
ITA :Immuno Turbidimetric assay
WB: Western Blot
IF: immunofluorescence
IP: Immuno precipitation
ELISA: Enzyme-linked Immunosorbent assay
IHC: Immunohistochemistry
FC: flow cytometry
生物危害 / Hazard/Biohazard
This antibody contains 0.09% sodium azide as preserva-tive. Please handle and dispose the product properly. No known biohazard is associated with this product.